
Figure 6. Change in plasma ammonia levels after long-term treatment with carglumic
acid48 (Reproduced from Burlina A, Cazzorla C, Zanonato E, et al, Clinical experience with
N-carbamylglutamate in a single-centre cohort of patients with propionic and methylmalonic
aciduria, Mol Genet Metab Rep 2016;8:34–40, © 2016 The Authors, under the CC BY-NC-ND
license (http://creativecommons.org/licenses/by-nc-nd/4.0/)