Figure 4. The relationship between protein prescription and symptoms in people with PA
or MMA: (a) protein intake as g/kg/day; (b) protein intake as percentage of recommended
daily allowance.14 (Adapted from Molema F, Gleich F, Burgard P, et al; additional individual
contributors from E-IMD, Evaluation of dietary treatment and amino acid supplementation
in organic acidurias and urea-cycle disorders: on the basis of information from a European
multicenter registry, J Inherit Metab Dis 2019;42:1162–75, © 2019 The Authors, under
the terms of the Creative Commons Attribution-NonCommercial License, https://creative
commons.org/licenses/by-nc/4.0/)