Figure 1. The biochemical pathways involved in pathogenesis of urea cycle disorders and organic acidurias.3 (Adapted from Häberle J, Chakrapani A, Ah Mew N, Longo N, Hyperammonaemia in classic organic acidaemias: a review of the literature and two case
histories, Orphanet J Rare Dis 2018;13:219, © The Author(s) 2018, under the terms of the Creative Commons Attribution 4.0 International License, http://creativecommons.org/licenses/by/4.0)